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Sub Subramony, MD : Research

Neuromuscular Medicine Specialist

Additional languages:
Hindi,
Malayalam,
Tamil
Photo of Sub Subramony

Research at a glance

Top areas of exploration

  • Spinocerebellar Ataxias , 30 publications
  • Friedreich Ataxia , 23 publications
  • Phenotype , 18 publications
  • Spinocerebellar Degenerations , 17 publications

Research activity

183 publications

9,381 citations

Why is this important?

Focus

My key research interests include phenotypic characterization, phenotype-genotype correlations and pathogenic mechansims in genetically induced cerebellar ataxias and muscular dystrophies. In addition, I also am interested in developing assessment methods, biomarker discovery and therapeutic modalities for such diseases.

Active clinical trials

END-DM1

Building on previous work of the Myotonic Dystrophy Clinical Research Network (DMCRN), the present study seeks to overcome insufficient data on natural history; lack of reliable biomarkers; and incomplete characterization and limited biological…

Investigator
Sub Subramony
Status
Accepting Candidates
Ages
18 Years - 70 Years
Sexes
All

My publications

183 publications

2021

Pain as a significant symptom in patients with periodic paralysis-A cross-sectional survey.

Muscle & nerve

•

2021

Safety and Efficacy of Omaveloxolone in Friedreich Ataxia (MOXIe Study)

Annals of Neurology

•

2021

Scoliosis in Friedreich's ataxia: longitudinal characterization in a large heterogeneous cohort

Annals of Clinical and Translational Neurology

•

2020

"Status myotonicus" in Nav1.4-M1592V channelopathy.

Neuromuscular disorders : NMD

•

2020

Dysphagia in spinocerebellar ataxias type 1, 2, 3 and 6.

Journal of the neurological sciences

•